Hypoplastic left heart syndrome (HLHS) is an important reason of deaths due to congenital heart diseases in newborns. The first step of palliative operations is generally performed between the first few days and two weeks of their lives to ensure circulatory balance. Patients not treated early are fatal. However, there are patients who can survive without surgical intervention. As in our 2-year-old patient with no growth retardation; protective mechanisms such as widely patent ductus arteriosus, adequate coronary circulation, restrictive atrial septal defect (ASD), normal pulmonary venous return and no significant arterial obstruction can make this possible.