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A CASE SERIES OF RARE AND AGGRESSIVE EXTRA CRANIAL MALIGNANT RHABDOID TUMORS.
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  • Sowmya J,
  • Prakruthi Kaushik,
  • Nuthan Kumar,
  • Arun Kumar,
  • Avinash T,
  • Arunakumari BS,
  • Appaji L
Sowmya J
Kidwai Memorial Institute of Oncology

Corresponding Author:[email protected]

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Prakruthi Kaushik
Kidwai Memorial Institute of Oncology
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Nuthan Kumar
Kidwai Memorial Institute of Oncology
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Arun Kumar
Kidwai Memorial Institute of Oncology
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Avinash T
Kidwai Memorial Institute of Oncology
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Arunakumari BS
Kidwai Memorial Institute of Oncology
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Appaji L
Kidwai Memorial Institute of Oncology
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Abstract

Malignant rhabdoid tumors (MRT) are very aggressive neoplasms seen in infantile age groups. A high index of suspicion is needed for early diagnosis. They are small round cell tumors with characteristic loss of INI -1 expression. Here we present a case series of 6 rhabdoid tumors diagnosed over 2 years, of which 4 of them presented as soft tissue swelling neck and chest wall. All of them had a very short duration of presentation and despite timely diagnosis, 4 of them progressed while on treatment and resulted in mortality.