Acute Aortic Syndrome in Marfan Syndrome with Chest Pain and Negative
Initial Imaging
- Sorush Rokui,
- Edward Percy,
- Joel Price
Abstract
A 25-year-old male with Marfan Syndrome and previous aortic root surgery
presented with severe chest and upper back pain. Initial CT angiogram
showed mild aortic dilatation but no acute dissection. Anti-impulse
therapy was initiated. Five days after presentation, follow-up CT
angiography revealed a new pseudoaneurysm of the descending thoracic
aorta. The patient underwent replacement of the mid-descending thoracic
aorta with a collagen-impregnated woven polyester tube graft without
complication. Despite negative initial imaging and relatively small
aortic size, patients with Marfan Syndrome with acute chest pain should
be treated with high suspicion and may benefit from admission and serial
imaging.