A Calcified Unicommissural Unicuspid Aortic Valve: is it the trigger to
the calcified amorphous tumor?
Unicommissural unicuspid aortic valve (UAV) is a rare valvular
malformation. It may lead to severe aortic stenosis with or without
aortic regurgitation. UAVs have many characteristic changes such as
premature dysmorphic valvular calcification and premature valvular
dysfunction. Transesophageal echocardiography (TEE) was described as the
gold standard for the diagnosis of UAVs. We reported the case of a 58
years old man who presented with syncope and dyspnea due to severe
aortic stenosis secondary to a heavily calcified unicommissural UAV.
After the surgery pathological specimen showed severe amorphous
calcification just like a calcified amorphous tumor (CAT).