Regression of kaposiform
lymphangiomatosis and chronic disseminated intravascular coagulation
after inhaled budesonide-formoterol treatment
Masaru Imamura1, Chansu Shin1,
Akihiko Saitoh1, Michio Ozeki 2,
Kentaro Matsuoka3 Chihaya Imai1
1Department of Pediatrics, Niigata University Graduate
School of Medical and Dental Sciences, Niigata, Japan
2Department of Pediatrics, Graduate School of
Medicine, Gifu University, Gifu, Japan
3Department of Pathology, Tokyo Metropolitan
Children’s Medical Center, Tokyo, Japan
Corresponding author: Masaru Imamura, Department of Pediatrics, Niigata
University Graduate School of Medical and Dental Sciences, 1-757
Asahimachi-dori, Chuou-ku, Niigata City, Niigata 951-8510, Japan.
Phone +81-25-227-2222
FAX +81-25-227-0778
Email: mimamura@med.niigata-u.ac.jp
Word Count for Main Text: 701 words
Number of Tables: 0
Number of Figures: 2
Running title: KLA IMPROVED AFTER INHALED STEROID
Keywords: kaposiform lymphangiomatosis, lymphatic malformation, inhaled
corticosteroid, rare disease, progressive disease
Abbreviations: