Regression of kaposiform lymphangiomatosis and chronic disseminated intravascular coagulation after inhaled budesonide-formoterol treatment
Masaru Imamura1, Chansu Shin1, Akihiko Saitoh1, Michio Ozeki 2, Kentaro Matsuoka3 Chihaya Imai1
1Department of Pediatrics, Niigata University Graduate School of Medical and Dental Sciences, Niigata, Japan
2Department of Pediatrics, Graduate School of Medicine, Gifu University, Gifu, Japan
3Department of Pathology, Tokyo Metropolitan Children’s Medical Center, Tokyo, Japan
Corresponding author: Masaru Imamura, Department of Pediatrics, Niigata University Graduate School of Medical and Dental Sciences, 1-757 Asahimachi-dori, Chuou-ku, Niigata City, Niigata 951-8510, Japan.
Phone +81-25-227-2222
FAX +81-25-227-0778
Email: mimamura@med.niigata-u.ac.jp
Word Count for Main Text: 701 words
Number of Tables: 0
Number of Figures: 2
Running title: KLA IMPROVED AFTER INHALED STEROID
Keywords: kaposiform lymphangiomatosis, lymphatic malformation, inhaled corticosteroid, rare disease, progressive disease
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