Introduction

Mucinous Tubular and spindle cell carcinoma (MTSCC) is a rare renal tumour with low potential for malignancy [1, 2-3]. It was included as a distinct entity in the World Health Organization classification in 2004 [4]. We report the case of an 80-year-old woman diagnosed incidentally with a left renal mass on an abdominal computed tomography scan. Histological examination revealed a kidney mucinous tubular and spindle cell carcinoma. The objective of our work is to report a rare entity of renal tumor whose knowledge by clinicians and pathologists is essential, because of its favorable prognosis compared to that of other renal cell carcinomas.