CONCLUSION
We described the case of an older patient with late-onset ARS syndrome who tested positive for anti-OJ and anti-Ro-52 antibodies. Interstitial pneumonia is an established complication of anti-ARS antibody syndrome, particularly when accompanied by positive anti-OJ antibodies. However, it can also result in rapid necrosis of the fingers without interstitial pneumonia. Prednisolone pulse therapy was remarkably effective, leading to the rapid cessation of disease progression. Detecting anti-OJ antibodies by immunoprecipitation is potentially more reliable than the LIA method. Information on the clinical course of this atypical ARS syndrome and treatment could contribute to the daily practice of rheumatology for clinicians.