Figure Legends:
Figure 1. A. Modified A4C view showing large sub-arterial VSD, B. Turbulence in outflow tract at valve level, C. Moderate truncal stenosis with peak gradient of 62mmHg, D. Mild-moderate truncal regurgitation seen on same view
Figure 2. Quadricuspid truncal valve in fully closed state, note the central AR jet through non-coapting leaflets [* denotes all leaflets]
Figure 3. A. Modified ductal view showing dilated ductal arch with sequential RPA (red arrow), LPA (orange arrow) branching, B. Ductal arch giving rise to RPA and LPA
Figure 4. A. Branching pattern in CT angiogram (LAO section) and 3D reconstructed CT (posterior view) correlation ( Note that ascending aorta is small and type B interrupted giving only right brachiocephalic artery and left common carotid artery); B. Expected normal arch and existing ductal arch shown; C. Cardiac CT coronal section showing right brachiocephalic artery and left common carotid artery arising from hypoplastic ascending aorta.
Figure 5. Schematic depiction of anatomy of the index case.
Figure 6. Post bilateral pulmonary artery banding showing significant gradients with functioning PA band