Figure Legends:
Figure 1. A. Modified A4C view showing large sub-arterial VSD, B.
Turbulence in outflow tract at valve level, C. Moderate truncal stenosis
with peak gradient of 62mmHg, D. Mild-moderate truncal regurgitation
seen on same view
Figure 2. Quadricuspid truncal valve in fully closed state, note the
central AR jet through non-coapting leaflets [* denotes all
leaflets]
Figure 3. A. Modified ductal view showing dilated ductal arch with
sequential RPA (red arrow), LPA (orange arrow) branching, B. Ductal arch
giving rise to RPA and LPA
Figure 4. A. Branching pattern in CT angiogram (LAO section) and 3D
reconstructed CT (posterior view) correlation ( Note that ascending
aorta is small and type B interrupted giving only right brachiocephalic
artery and left common carotid artery); B. Expected normal arch and
existing ductal arch shown; C. Cardiac CT coronal section showing right
brachiocephalic artery and left common carotid artery arising from
hypoplastic ascending aorta.
Figure 5. Schematic depiction of anatomy of the index case.
Figure 6. Post bilateral pulmonary artery banding showing significant
gradients with functioning PA band