INTRODUCTION
Lymphatic malformations (LMs) are the second most common type of
vascular malformation(12%), following by venous
malformations(70%)[1]. Primary vaginal lymphatic
malformation is an extremely rare category of LMs. Due to atypical
clinical manifestations and difficulties of differential
diagnosis,vaginal lymphatic malformation could be easily misdiagnosed or
neglected. Here,we reported the first Chinese case of primary vaginal
and pelvic LMs who was diagnosed in childhood.The patient presented with
chronic increased vaginal discharge as well as white granular
projections in the hymen.There was a 4-year interval from the
manifestation to the verified diagnosis.
Modern imaging technologies and refined interventional treatment
strategies are now central parts in the multidisciplinary management of
the LMs patients[2].In this case, for the very
first time, we tried to utilize sclerotherapy with Bleomycin combined
with oral Sirolimus to control the progress of microcystic vaginal
lymphatic malformation in children.The results turned out to be
desirable.