INTRODUCTION

Lymphatic malformations (LMs) are the second most common type of vascular malformation(12%), following by venous malformations(70%)[1]. Primary vaginal lymphatic malformation is an extremely rare category of LMs. Due to atypical clinical manifestations and difficulties of differential diagnosis,vaginal lymphatic malformation could be easily misdiagnosed or neglected. Here,we reported the first Chinese case of primary vaginal and pelvic LMs who was diagnosed in childhood.The patient presented with chronic increased vaginal discharge as well as white granular projections in the hymen.There was a 4-year interval from the manifestation to the verified diagnosis.
Modern imaging technologies and refined interventional treatment strategies are now central parts in the multidisciplinary management of the LMs patients[2].In this case, for the very first time, we tried to utilize sclerotherapy with Bleomycin combined with oral Sirolimus to control the progress of microcystic vaginal lymphatic malformation in children.The results turned out to be desirable.