Introduction:
Lymphangioma benign and slow-growing tumors of vascular origin that can be congenital or acquired (1). When congenital these can occur in isolation or can be a part of various syndromes (Turner, Noonan, Downs). When acquired, they are mostly a result of infection, inflammation, or cancer that can block the normal lymphatic flow (2). Lymphangiomas are rare, representing 4% of vascular neoplasms in general and approx. 25% of all nonmalignant tumors of vascular etiology in the pediatric age group. They almost always exist at birth, but overt presentation depends on the rate of growth in which fluid accumulates and on the site of its origin. 90% of these tumors occur in children, and 90% of children are <2 years of age at the time of presentation. Abdominal lymphangiomas are very rarely seen and pancreatic lymphangiomas are rarest. Pancreatic lymphangiomas compose <1% of all pancreatic neoplasms. These are mostly found in women. Here we discuss a case where a young man presented to us with epigastric pain and workup led us to the diagnosis of pancreatic lymphangioma.