Introduction:
Lymphangioma benign and slow-growing tumors of vascular origin that can
be congenital or acquired (1). When congenital these can occur in
isolation or can be a part of various syndromes (Turner, Noonan, Downs).
When acquired, they are mostly a result of infection, inflammation, or
cancer that can block the normal lymphatic flow (2). Lymphangiomas are
rare, representing 4% of vascular neoplasms in general and approx. 25%
of all nonmalignant tumors of vascular etiology in the pediatric age
group. They almost always exist at birth, but overt presentation depends
on the rate of growth in which fluid accumulates and on the site of its
origin. 90% of these tumors occur in children, and 90% of children are
<2 years of age at the time of presentation. Abdominal
lymphangiomas are very rarely seen and pancreatic lymphangiomas are
rarest. Pancreatic lymphangiomas compose <1% of all
pancreatic neoplasms. These are mostly found in women. Here we discuss a
case where a young man presented to us with epigastric pain and workup
led us to the diagnosis of pancreatic lymphangioma.