Conclusion
In case of midline defects accompany by hypernatremia, seizures, polyuria with or without developmental delay, the brain should be imaged to confirm its morphology and investigation of associated endocrinologic dysfunctions should be suspected.
Keywords : Diabetes Insipidus, Cleft lip, Cleft palate, Midline defect, Holoprosencephaly

List of abbreviations:

DI: Diabetes Insipedus
CDI: Central Diabetes Insipedus
HPE: Holoprosrncephaly
MRI: Magnetic Resonance Imaging
ADH: Anti Diuretic Hormone
aDAVP: Desmpressine
PFO: Patent Foramen Ovale
PDA: Patent Dactus Artriosus
VSD: Ventricular Septal Defect
AVP: Arginin-Vasopressin