Introduction
Inflammatory myofibroblastic tumor
(IMT) is a rare mesenchymal tumor
tends to be locally invasive or recurrent and rarely metastasizes.
Originally described in the lung, and now has been reported at multiple
extrapulmonary sites, particularly shows a preference to visceral soft
tissue in children and young people.1 IMT of the
urinary system occurs mostly in the bladder. However, kidney IMT
represents a challenging diagnostic entity due to its nonspecific
clinical presentation, laboratory findings, and most importantly
radiologic findings.2 It is especially difficult to
distinguish renal IMT from malignant tumor before surgery in
children.3 Therefore, the awareness of its existence
and deep understanding of its clinical and imaging characteristics are
essential to avoid misdiagnosis and to provide better management.
Despite the uncertain biological behavior of IMT, most patients get a
favorable prognosis after surgery.4Herein, we report an IMT in a
6-year-old boy that was misdiagnosed as Wilms’ tumor. Written informed
consent for academic use of his information was obtained from the
children’s parents.