Introduction
In younger patients Lamin heart disease is an underdiagnosed etiology of complex irregular atrial arrhythmias occurring in the absence of pulmonary vein activity. As these arrhythmias can be impossible to map by serial contact mapping, we describe the use of a novel noncontact mapping array to characterize the septal origin of these atrial flutters, close to the site of conduction system disease in two sisters with Lamin A/C mutation. In addition, very unusual morphological abnormalities such as ventricular noncompaction and abnormal pulmonary vein connection are reported for the first time in Lamin heart disease.