Tetralogy of Fallot Associated with a Rare Type Partial Anomalous
Pulmonary Venous Return
Tetralogy of Fallot (TOF) is rarely associated with partial anomalous
pulmonary venous return (PAPVR). Unidentified PAPVR, however, might
increase the risk of pulmonary valve replacement in repaired TOF
patients by right ventricular (RV) dilatation and RV dysfunction. Here,
we present a case of a 19-year-old male who received a correction of TOF
18 years ago and a rare type of PAPVR was identified during the follow
up period. The anomalous pulmonary veins were connected to the left
hepatic vein, left superior vena cava, and the right superior vena cava.
Performing a pulmonary valve replacement, PAPVR was also corrected by an
intra-atrial baffle with a new approach using the venous plexus between
the left hepatic vein and the right hepatic vein.