Table 1. Characteristics of Individuals with Two Potentially
Pathogenic CFTR Variants.
Definitions of abbreviations are as follows: CFTR=cystic fibrosis
transmembrane regulator gene, LABA=long acting beta agonist, ICS=inhaled
corticosteroid, ER=emergency room, NA=No information available,
FEV1=forced expiratory volume in 1 second, FVC=forced vital capacity.