CFTR Genotype
F508del/ 5T;TG12 5T;TG12/ 5T;TG12 F508del/ 5T;TG12 F508del/ Arg1070Trp
Age (years) 30 24 69 59
Age of asthma onset (years) 22 6 6 5
Sex Female Female Female Female
Pre-bronchodilator FEV1% predicted 65% 77% 51% 77%
Post-bronchodilator FEV1% predicted
78%
113%
63%
NA
Pre-bronchodilator FEV1/FVC 0.72 0.58 0.67 0.88
Treated with LABA+ICS Yes No Yes Yes
Hospitalization last 12 months No No No No
Lifetime Hospitalization No NA Yes No
ER visit last 12 months No Yes No No
Unscheduled outpatient visit last 12 months Yes Yes Yes Yes
Corticosteroid burst last 12 months No No No No
Diabetes No No No Yes