N°1, Masuda et al, 1994
|
29
|
F
|
Asthma (prior to the diagnosis of SS)
|
Pruritic papules and plaques on face, neck, trunk and extremities
Temperature: 37.7°C
|
Dense dermal infiltrate
With multiple neutrophils and eosinophils.
|
Good evolution after the
administration of 50 mg/day of dapsone.
Recurrence of lesions 2 years after the first episod
Prolonged treatment with Prednisolone
(10 mg/day) and dapsone (100 mg/day)
|
Respiratory tract infection
|
N°2, Masuda, et al, 1994
|
61
|
M
|
None
|
Red papules and plaques
necrotic center on face, neck and back.
Fever : 39.3°C
|
Half of the cell
infiltrate composed of neutrophils, eosinophils
10%.
|
Complete healing after 2 weeks of treatment with potassium iodide
(l g/day)
Recurrence at 2 months after the therapy, resolving under the same
treatment for 7 days
|
None
|
N°3, Soon et al, 2016
|
90
|
M
|
Severe refractory celiac disease (Prior to the SS)
Enteropathy-associated T-cell lymphoma (With the onset of SS)
|
Diffuse pink, oedematous,
papules, nodules, and plaques
on the back,
buttocks
and abdomen.
Fever: 38.2°C
|
Superficial and mid-dermal perivascular
and interstitial infiltrate with
numerous eosinophils
|
Spread of the eruption
Recurrent gastro-intestinal bleeding leading to death
|
None
|
Our case
|
65
|
F
|
Chronic lymphocytic leukaemia (2 years before the onset of SS)
|
Multiple erythematous and painful cutaneous lesions
Fever (38.5°C)
|
Inflammatory infiltrate rich in eosinophilic polynuclear cells
|
Good evolution under doxycyline 100mg/day and high-level-topical
corticosteroid for 10 days
(no recurrence with a follow-up for 2 years)
|
Insecte bite
|