Case, Author and Year of publication
Age (years)
Sex
Medical history/ Associated disease
Clinical presentation
Histology
Evolution
Triggering factor
N°1, Masuda et al, 1994
29
F
Asthma (prior to the diagnosis of SS)
Pruritic papules and plaques on face, neck, trunk and extremities Temperature: 37.7°C
Dense dermal infiltrate With multiple neutrophils and eosinophils. Good evolution after the administration of 50 mg/day of dapsone. Recurrence of lesions 2 years after the first episod Prolonged treatment with Prednisolone (10 mg/day) and dapsone (100 mg/day)
Respiratory tract infection
N°2, Masuda, et al, 1994
61
M
None
Red papules and plaques necrotic center on face, neck and back. Fever : 39.3°C Half of the cell infiltrate composed of neutrophils, eosinophils 10%. Complete healing after 2 weeks of treatment with potassium iodide (l g/day) Recurrence at 2 months after the therapy, resolving under the same treatment for 7 days
None
N°3, Soon et al, 2016
90
M
Severe refractory celiac disease (Prior to the SS) Enteropathy-associated T-cell lymphoma (With the onset of SS) Diffuse pink, oedematous, papules, nodules, and plaques on the back, buttocks and abdomen. Fever: 38.2°C Superficial and mid-dermal perivascular and interstitial infiltrate with numerous eosinophils Spread of the eruption Recurrent gastro-intestinal bleeding leading to death
None
Our case
65
F
Chronic lymphocytic leukaemia (2 years before the onset of SS)
Multiple erythematous and painful cutaneous lesions Fever (38.5°C)
Inflammatory infiltrate rich in eosinophilic polynuclear cells
Good evolution under doxycyline 100mg/day and high-level-topical corticosteroid for 10 days (no recurrence with a follow-up for 2 years)
Insecte bite