Figures legend:
Figure 1: Photograph of buccal mucosa pigmentations (arrow).
Figure 2: Abdominal CT scan and upper gastrointestinal series showing polypoid lesions inside the intestinal lumen (arrow).
Figure 3: Intraoperative view of intestinal lesions (arrow).
Figure 4: Histology image, showing the excised jejunal Peutz-Jeghers polyp. A: Polyp with hyperplastic foveolar epitheluim and inflammatory stroma with some cords of smooth muscle (→) (HEx25) B: Polyp with inflammatory stroma, smooth muscle fibres (→), and non-dysplastic hyperplastic foveolar epitheluim (HEx200)
Figure 5: Gastric polyp at endoscopy (arrow).