Manuscript:
Introduction :
Peutz–Jeghers syndrome (PJS) is a rare but well-described
inherited disease, characterized by specific pigmented freckle-like
mucocutaneous lesions, and gastrointestinal and extra gastrointestinal
hamartomatous polyps. The most common and concerning manifestation in
children and adolescents is the occurrence of small bowel
intussusception which could represent a serious surgical emergency and
be life-threatening (1,2).
We report in this paper the case of recurrent intestinal
intussusceptions in a child, resulting of hamartomatous Peutz Jeghers
polyps. Our aim is to remind diagnostic and management particularities
of this unusual condition and to highlight the importance of regular
follow-up for these patients to avoid complications.