INTRODUCTION
Unilateral absence of pulmonary artery (UAPA) is a group congenital
heart defect of complete absence of the intra-pericardial segment of one
main pulmonary artery branch [1]. UAPA can exist alone or combined
with other intracardiac malformations. About 0.95% to 3.23% of
Tetralogy of Fallot (TOF) is combined with UAPA, and approximately 100
cases have been reported in the literature before 2014 [1,2]. The
management of TOF combined with UAPA is still very controversial.
According to the indications of classic TOF correction, it is difficult
to reach the criteria of one-stage correction with McGoon
index>1.2. The literature reported that the vast majority
of such patients are treated with palliative surgery or unilateral
pulmonary artery reconstruction (single-lung repair) instead of
bilateral pulmonary artery reconstruction (two-lung repair) [1, 3,
4].
In this study, we reviewed the bilateral pulmonary reconstruction in
patients with TOF combined with UAPA at our institute and discussed the
therapeutic effect of this strategy.