INTRODUCTION
Unilateral absence of pulmonary artery (UAPA) is a group congenital heart defect of complete absence of the intra-pericardial segment of one main pulmonary artery branch [1]. UAPA can exist alone or combined with other intracardiac malformations. About 0.95% to 3.23% of Tetralogy of Fallot (TOF) is combined with UAPA, and approximately 100 cases have been reported in the literature before 2014 [1,2]. The management of TOF combined with UAPA is still very controversial. According to the indications of classic TOF correction, it is difficult to reach the criteria of one-stage correction with McGoon index>1.2. The literature reported that the vast majority of such patients are treated with palliative surgery or unilateral pulmonary artery reconstruction (single-lung repair) instead of bilateral pulmonary artery reconstruction (two-lung repair) [1, 3, 4].
In this study, we reviewed the bilateral pulmonary reconstruction in patients with TOF combined with UAPA at our institute and discussed the therapeutic effect of this strategy.