What’s Already Known About This Topic? What Does This Study Add?
There are no publications linking prenatally-detected severe oligohydramnios that self-corrects upon birth in RCS patients. We report two generations of RCS, flagged prenatally, with resolving severe oligohydramnios. This report suggests that self-resolving oligohydramnios is an early sign of malfunctioning kidney in RCS individuals and demonstrates how a genetic diagnosis impacted patient management.