Introduction:
Pulmonary artery sarcomas (PASs) are the most common primary tumors of
the pulmonary artery (PA), but the incidence of this diagnosis is
extremely rare. PASs is predominantly presented among patients from
their third to seventh decade, with an average age of 49 years. PASs are
always highly malignant, women are involved twice as often as men. The
most common clinical manifestation of PASs is dyspnea (72%) followed by
chest pain (45%), cough (42%), and hemoptysis (24%). Systematic
symptoms of PASs are less rare and they include weight loss (21%),
syncope (9%), and fever (8%). The presence of these symptoms often
causes misdiagnosis of pulmonary thromboembolism (PTE) (1-3).