Conclusion
With the development of new surgical methods for the treatment of SV heart defects, it is important to understand the long-term outcomes for patients who have not been operated on.29While the Fontan operation has become a common and effective method for SV treatment, long-term outcomes are fraught with morbidity and mortality . The majority of patients in our series and in the literature to demonstrate advanced survival had DILV and PS.In our opinion,such patients with balanced hemodynamic condition should be followed and treated conservatively. Major cardiac surgery which leads to gross hemodynamic adjustments should be avoided.30 The optimal timing for surgery and appropriate surgical method can be determined based on: 1) the patient’s symptoms and specific diagnosis of SV heart defect, and 2) the following conditions: the anatomy of the parting and concurrent heart malformations, the development of the PA, the amount of pressure and resistance, and ventricular function, with a significant aim to reduce mortality and improve the prognosis as well as quality of life of SV patients.