INTRODUCTION
The development of a lymphatic leak in the pleural space (chylous
effusion or chylothorax) or in the abdominal cavity (chylous ascites) is
a rare and life-threatening presentation. Although chylous effusions and
ascites can occur secondary to surgical or traumatic processes, this
discussion focuses on non-traumatic, congenital disorders of pulmonary
or intestinal lymphatic flow that result in symptomatic lymphatic leak.
Early detection of a primary lymphatic disorder improves outcome and
reduces complications. Without prospective trials to guide care, we
present our multidisciplinary approach to the diagnosis and treatment of
congenital chylous effusions and ascites.