Conclusion:
DT in the pancreas is exceedingly rare form of already rare
intraabdominal form desmoid type fibromatosis. by virtue of nonspecific
clinical presentation or asymptomatic incident mass discovered DT
diagnosis is considered challenging, secondly, the lack of specific
clinical investigation. immunohistochemical staining is the main
pathological diagnosis positive in β-catenin nuclear or negative as in
S100 protein.
Radical-margin-free surgical resection remains the mainstay management
approach while chemotherapy and/or radiotherapy are not effective and no
standardized protocol of consensuses and considered the last resort for
only high risk for or advance cases.
long-term follow up is warranted. Due to recurrence behaviour of the
tumour.
According to midline English literature our case presents the largest
pancreatic DT fibromatosis to be published.