Case Presentation:
A case of a 42 years old African-origin male who were medically free
apart from recurrent left upper abdominal pain for more than 10 years,
and no significant past surgeries, trauma, or cancer history in his
family. By physical examination, the patient has a non-tender large
abdominal mass at left hypochondrial area extending down to the pelvis
below the umbilicus with rigid and smooth surface. The computed
tomography scan showed large heterogenous mass which appears to be of
pancreatic origin (the body and tail cannot be visualized due to this
mass measuring about 23 cm by 15 cm by11 cm. The patient underwent
radical en-mass resection with extended left pancreatectomy, segmental
transverse colectomy, splenectomy, adrenalectomy, and subsequent
colo-colic anastomosis. Histopathology and immunohistochemistry
confirmed the diagnosis of pancreas fibromatosis desmoid- type. The
follow up for the patient completed up to 5 years and no recurrence
clinically or by ultrasound demonstrated.
Conclousion : our case is a rare and uniquely the largest
pancreatic desmoid-type fibromatosis to be reported in the literature
with curative resection despite being locally invasive to adjacent
organ.