Case Presentation:
A case of a 42 years old African-origin male who were medically free apart from recurrent left upper abdominal pain for more than 10 years, and no significant past surgeries, trauma, or cancer history in his family. By physical examination, the patient has a non-tender large abdominal mass at left hypochondrial area extending down to the pelvis below the umbilicus with rigid and smooth surface. The computed tomography scan showed large heterogenous mass which appears to be of pancreatic origin (the body and tail cannot be visualized due to this mass measuring about 23 cm by 15 cm by11 cm. The patient underwent radical en-mass resection with extended left pancreatectomy, segmental transverse colectomy, splenectomy, adrenalectomy, and subsequent colo-colic anastomosis. Histopathology and immunohistochemistry confirmed the diagnosis of pancreas fibromatosis desmoid- type. The follow up for the patient completed up to 5 years and no recurrence clinically or by ultrasound demonstrated.
Conclousion : our case is a rare and uniquely the largest pancreatic desmoid-type fibromatosis to be reported in the literature with curative resection despite being locally invasive to adjacent organ.