Discussion
Our patient developed cancer at the age of 75. The primary treatment option is surgery and in the advanced stage of the disease, due to the small number of cases, there are no recommendations for systemic therapy . Examples of chemotherapy based on platinum preparations (3), fluorouracils (4) and taxanes are given in the literature. In our case, the patient had a positive response only to the third line of chemotherapy, FOLFIRI3 regimen plus Sandostatin LAR, which emphasizes the importance of early evaluation of the clinical response and changes in chemotherapy at the first progression of the disease. No data on the radiosensitivity of this tumor were found in the reviewed literature, so we did not decide to use radiotherapy in the treatment of our patient.