1 INTRODUCTION
Acalvaria is a rare congenital malformation characterized by the absence of the cranial vault bones, the dura mater and associated muscles.1 Although the basal and facial bones are normally developed, the cranial content can often be abnormal.1-3 Its pathogenesis is not well known, but the abnormality occurring after neurulation is the most accepted theory.1-3 It is a fatal condition with only a few cases of survivors often with severe neurological disorders.1-4 To date, only one case has been reported in Africa.5 We report a new surviving case presenting with facial dysmorphia and hemiparesis.