Introduction
Unilateral absence of a pulmonary artery is a rare congenital heart
disease,1 coexisting with other cardiovascular
malformations, that in an isolated form are located contralateral to the
aortic arch, with RPA being the most commonly
affected.2,3
Patients may present with hemoptysis, recurrent respiratory infections,
pulmonary hypertension or congestive heart failure,2 a
comprehensive imaging evaluation, such as computed tomography, will
allow to determine the therapeutic strategy, which may be a
systemic-to-pulmonary shunt until direct reconstruction is
advisable.4 Recent reports recommend a hybrid
strategy, placing an intraductal stent and subsequential surgical
reconstruction.5
We present two cases that were approved by the local institutional
review board. The approval included a waiver of informed consent because
it does not show personal data of patients.