Introduction
Unilateral absence of a pulmonary artery is a rare congenital heart disease,1 coexisting with other cardiovascular malformations, that in an isolated form are located contralateral to the aortic arch, with RPA being the most commonly affected.2,3
Patients may present with hemoptysis, recurrent respiratory infections, pulmonary hypertension or congestive heart failure,2 a comprehensive imaging evaluation, such as computed tomography, will allow to determine the therapeutic strategy, which may be a systemic-to-pulmonary shunt until direct reconstruction is advisable.4 Recent reports recommend a hybrid strategy, placing an intraductal stent and subsequential surgical reconstruction.5
We present two cases that were approved by the local institutional review board. The approval included a waiver of informed consent because it does not show personal data of patients.