Introduction
Unicuspid aortic valve (UAV) is an infrequent congenital anomaly secondary to altered aortic cusp development from tubercles1. A disordered number of cusps results from fusion or duplication, with a reported occurrence with echocardiography of 1% for bicuspid aortic valve (BAV), 0.05% for quadricuspid aortic valve, and 0.02% for UAV2. Due to its rarity, clinical progression and complications of UAV are not well known.