Abstract
Mitral annular disjunction (MAD) is a structural abnormality of the
mitral annulus, defined by a detachment of the atrial wall-mitral
valvular junction from the left ventricular (LV) free wall.
This structural abnormality in mitral annulus fibrosus is significantly
associated with the presence of mitral valve prolapse (MVP) [1], but
it can be also detected in normal cases as an anatomical variation of
the mitral annulus fibrosus [2]. The main tools to detect MAD are
echocardiography and cardiac magnetic resonance. Prevalence of MAD in
the general population ranges from 7% [1] to 9% [2].
Several studies proved an association between MAD and arrhythmic events,
independently of concomitant mitral valve abnormalities, suggesting the
existence of a novel entity: MAD arrhythmic syndrome [3].
Herein we describe a case report of a middle age man with MAD who
experienced ventricular arrhythmias and placement of an implantable
cardioverter-defibrillator (ICD).
Keywords : Mitral annular disjunction, ventricular arrhythmias,
echocardiography, cardiac magnetic resonance