1 | INTRODUCTION
Treatment of patients associated with FSV and TAPVC has a high mortality
rate and poor prognosis1-4. Patients with FSV and
TAPVC often have visceral heterotaxy syndrome3,5,6,
which may led to a worse clinical outcomes. In addition, Pulmonary
atresia2,7, pulmonary artery
stenosis3, preoperative PVO1,7,
right ventricular dominance3,8, infracardiac or mixed
TAPVC7 , low weight and younger age9are considered risk factors that increase the mortality of these
patients.
In fact, in 1999, J. William Gaynor and his
colleagues10 performed an autopsy on similar patients.
Lung tissue was used for histopathological examination. It was found
that pulmonary vein wall was very thick, and elastic tissue staining
demonstrated elastic tissue in the pulmonary vein wall and
arterialization of pulmonary veins. This pathological change of
pulmonary veins may lead to increased pulmonary vascular resistance.
This may explain why patients with FSV combined with TAPVC have a poor
prognosis.
We retrospectively analyzed mid-term results and risk factors of
petients with FSV and TAPVC in our center.