Introduction
Desmoplastic Small Round Cell Tumor (DSRCT) is a rare neoplasm that affects mainly adolescent and young adult males. This tumor presents with a polyphenotypic differentiation profile, showing muscular, neural and epithelial markers and carries the recurrent chromosomal translocation t(11;22)(p13;q12)1,2 . Abdomen/pelvis are the major sites of growth and the prognosis is poor, but data from literature shows that patients with paratesticular DSRCT have better outcomes2-4 . We present the fifth case of primary DSRCT of the testis described in literature and discuss these locations as a prognostic factor.