Biologicals used in HLH Mechanism of action Specially used in:
Rituximab CD 20 antibody EBV associated HLH
Anakinra IL-1 receptor antagonist sJIA associated HLH
Alemtuzumab CD 52 antibody Serotherapy in HSCT for HLH
Tocilizumab IL-6 receptor antagonist Trials ongoing
Ruxolitinib JAK 1,2, receptor antagonist Trials ongoing
Emapalumab IFN gamma antibody Trials ongoing
Adalimumab TNF alpha inhibitor Post-transplant associated HLH