Introduction
Patients with pulmonary atresia and ventricular septal defect (PA/VSD) show a variety of pulmonary and coronary artery anatomies [1]. Additionally, a coronary pulmonary artery fistula (CPAF) occurs in <10% of patients with PA/VSD [2]. Various types of CPAF associated with PA/VSD have been reported, however, to the best of our knowledge, there is no report of prenatal diagnosis of CPAF with PA/VSD, probably due to the rarity of the condition and the technical difficulty of the imaging method. In this report, we demonstrated clear images of CPAF associated with PA/VSD using fetal echocardiography and confirmed the exact morphology of CPAF in a neonate using electrocardiography (ECG)-gated 320-row computed tomography (CT) in neonate.