Case Report:
Informed consent was obtained from the child and her parents for the purpose of publication of her data. An 11-year-old girl presented to our clinic with exertional dyspnea, severe central cyanosis and digital clubbing with resting saturations of 70% while breathing room air. Her 2D echocardiography-color Doppler evaluation revealed tricuspid atresia, pulmonary atresia, normally related great arteries, absence of confluence with severe LPA stenosis at its origin. Her computer tomography angiogram showed the MPA to be continuous with the RPA without any connection to LPA with only a chord of tissue between both ends measuring about 10 mm. The LPA was supplied by a patent ductus arteriosus. The hilar LPA measured 14mms. (Figure 1A, 2A).