Abstract
Total anomalous pulmonary venous connection (TAPVC) is an anomaly where the pulmonary veins are directly connected to one of the systemic veins or to the right atrium. The most common classification of this condition is by Craig, Darling and Rothney, which is based on the anatomic site of the abnormal connection. A few variants are reported which do not fit into these classic forms.
We report 2 cases that previously underwent surgical repair of supracardiac TAPVC, where the pulmonary veins drained into the innominate vein through an ascending vertical vein. However these cases did not fit into the classic forms, because in both cases, a second vertical vein was detected incidentally during a follow-up diagnostic catheterization 1 year after the initial surgery. The second veins originated proximal to the ligated vertical vein and drained into the superior vena cava through the accessory hemiazygos vein and azygos vein.
In Case 1, which was did not provoke right heart volume overload and general condition is good. the patient is followed up carefully, even in the absence of any intervention or surgical intervention.
In Case 2, we confirmed right heart volume overload, and then performed coil embolization of the veno-venous shunt (VV shunt) of the second vertical vein.
This report describes a successful intervention by catheterization in the treatment of a VV shunt of TAPVC.