Abstract
Total anomalous pulmonary venous connection (TAPVC) is an anomaly where
the pulmonary veins are directly connected to one of the systemic veins
or to the right atrium. The most common classification of this condition
is by Craig, Darling and Rothney, which is based on the anatomic site of
the abnormal connection. A few variants are reported which do not fit
into these classic forms.
We report 2 cases that previously underwent surgical repair of
supracardiac TAPVC, where the pulmonary veins drained into the
innominate vein through an ascending vertical vein. However these cases
did not fit into the classic forms, because in both cases, a second
vertical vein was detected incidentally during a follow-up diagnostic
catheterization 1 year after the initial surgery. The second veins
originated proximal to the ligated vertical vein and drained into the
superior vena cava through the accessory hemiazygos vein and azygos
vein.
In Case 1, which was did not provoke right heart volume overload and
general condition is good. the patient is followed up carefully, even in
the absence of any intervention or surgical intervention.
In Case 2, we confirmed right heart volume overload, and then performed
coil embolization of the veno-venous shunt (VV shunt) of the second
vertical vein.
This report describes a successful intervention by catheterization in
the treatment of a VV shunt of TAPVC.