Conclusion
Cardiac leiomyosarcoma is an extremely rare tumor with a poor prognosis, and frozen section guided complete resection is the key to the treatment. Adjuvant chemoradiotherapy may further prolong survival and regular echocardiography should be followed up after the operation. The right submammarian thoracotomy approach has the advantages of its less invasive nature and suitability for complete tumor resection with lobectomy.