Introduction
Cardiac tumors are a very rare condition with a frequency of 0.02%. The prevalence ranges from 0.001% to 0.3%, and only 25% is malignant (1). The most common histological types are angiosarcomas, followed by rhabdomyosarcomas, mesotheliomas, and fibrosarcomas.
Leiomyosarcoma appears for less than 1% of cases (1). Despite aggressive multidisciplinary treatment including surgery, chemotherapy, and radiotherapy, the prognosis is poor, with median survival about 12 months (2,3,4). Metastasis is familiar, and up to 60% of cases have metastasis at the time of diagnosis (3). Adequate surgical resection, which may require lung resection ranging from lobectomy to pneumonectomy, is the mainstay of the treatment.
Clinical presentation is nonspecific; this makes early diagnosis difficult, and most cases are diagnosed on histology specimens and at autopsy. It is twice as common in females; the average age of occurrence is 45 years (range, 6 weeks to 77 years) (5).
In this case report, we present a successful management of leiomyosarcoma in a young lady.