Introduction
Cardiac tumors are a very rare condition with a frequency of 0.02%. The
prevalence ranges from 0.001% to 0.3%, and only 25% is malignant (1).
The most common histological types are angiosarcomas, followed by
rhabdomyosarcomas, mesotheliomas, and fibrosarcomas.
Leiomyosarcoma appears for less than 1% of cases (1). Despite
aggressive multidisciplinary treatment including surgery, chemotherapy,
and radiotherapy, the prognosis is poor, with median survival about 12
months (2,3,4). Metastasis is familiar, and up to 60% of cases have
metastasis at the time of diagnosis (3). Adequate surgical resection,
which may require lung resection ranging from lobectomy to
pneumonectomy, is the mainstay of the treatment.
Clinical presentation is nonspecific; this makes early diagnosis
difficult, and most cases are diagnosed on histology specimens and at
autopsy. It is twice as common in females; the average age of occurrence
is 45 years (range, 6 weeks to 77 years) (5).
In this case report, we present a successful management of
leiomyosarcoma in a young lady.