Screening was then completed independently by two members of the research team (FG-G and JLS-C) according to our inclusion criteria. Finally, XX sources were included for complete analysis.
 
Due to time and funding limitations, only studies published in English prior to March 2018 were included. Finally, the authors of the studies were not contacted due to time limitations. The literature search and title and abstract filtering were carried out by two researchers (XX and XX). 
Data charting
Of each study finally included the following variables were collected: year of publication, specialty, country, number of patients included, age, gender, type of study, type of publication, follow-up performed, main outcome, drugs, reported efficacy, type of CAPS (FCA, MWS, CINCA, overlap syndrome FCA-MWS, MWS-CINCA, undifferentiated, not informed), mutation studied, if applicable, language of the publication and inclusion / exclusion criteria.