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An unusual case of chronic and reversable pulmonary hypertension
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  • Paola del Coromoto Leon Suárez,
  • Iñigo Rúa-Figueroa Fernández de Larrinoa,
  • Stefano Urso,
  • Jose Domingo Marín Esmenota,
  • Eliú Nogales,
  • Francisco Portela
Paola del Coromoto Leon Suárez
Hospital Universitario de Gran Canaria Dr Negrin

Corresponding Author:[email protected]

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Iñigo Rúa-Figueroa Fernández de Larrinoa
Dr Negrin University Hospital of Gran Canaria
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Stefano Urso
Hospital Dr Negrín
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Jose Domingo Marín Esmenota
Hospital Universitario de Gran Canaria Dr Negrin
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Eliú Nogales
Hospital Universitario Insular de Gran Canaria
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Francisco Portela
Hospital Universitario de Gran Canaria Dr Negrin
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Behcet’s Disease (BD) is currently classified as “variable vessel vasculitis” (Chapel Hill, 2012). It is a chronic, multisystemic, inflammatory rheumatic disease. Its main manifestations are mucocutaneous, neurological, cardiovascular, pulmonary and musculoskeletal. Vascular involvement of BD, so-called “angio-Behcet”, appears in 7%-29% of patients. Arterial complications, such as arterial stenoses, pseudoaneurysms, and ruptures occur in a 1-14% range and represent a major cause of morbidity and mortality in BD patients. We, herein, report the case of a large aortic pseudoaneurysm producing severe pulmonary hypertension in a patient with angio-Behcet who had previously undergone aortic root replacement.