Abernethy malformation with multiple visceral aneurysms: An incidentally
detected rare disorder
Abernethy malformation is a rare congenital vascular anomaly
characterized by the portal vein’s congenital absence and accompanying
portosystemic shunts. This malformation is divided into two subgroups
depending on the superior mesenteric and splenic veins’ drainage to the
inferior vena cava. Abernethy malformation may cause portal
hypertension, hepatic encephalopathy, pulmonary hypertension, and heart
failure in patients later in life. Therefore, it is essential to
recognize this anomaly and follow up regarding these complications.
Moreover, other vascular anomalies and liver masses associated with
Abernethy malformation are rarely seen. Herein, we aimed to present a
rare adult case of Abernethy malformation with multiple saccular
visceral (hepatic, splenic, and renal artery) aneurysms diagnosed
incidentally on abdominal computed tomography. We aimed to emphasize the
radiological and clinical findings of this rare disorder.