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Abernethy malformation with multiple visceral aneurysms: An incidentally detected rare disorder
  • Ayşe Rüksan Ütebey,
  • Muhammed Rasid Aykota,
  • Furkan Ufuk
Ayşe Rüksan Ütebey
Pamukkale University

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Muhammed Rasid Aykota
Pamukkale University
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Furkan Ufuk
Pamukkale University
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Abstract

Abernethy malformation is a rare congenital vascular anomaly characterized by the portal vein’s congenital absence and accompanying portosystemic shunts. This malformation is divided into two subgroups depending on the superior mesenteric and splenic veins’ drainage to the inferior vena cava. Abernethy malformation may cause portal hypertension, hepatic encephalopathy, pulmonary hypertension, and heart failure in patients later in life. Therefore, it is essential to recognize this anomaly and follow up regarding these complications. Moreover, other vascular anomalies and liver masses associated with Abernethy malformation are rarely seen. Herein, we aimed to present a rare adult case of Abernethy malformation with multiple saccular visceral (hepatic, splenic, and renal artery) aneurysms diagnosed incidentally on abdominal computed tomography. We aimed to emphasize the radiological and clinical findings of this rare disorder.