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Cystic Fibrosis Liver Disease: Endovascular, endoscopic and surgical considerations
  • Sirish K. Palle,
  • Daniel H. Leung
Sirish K. Palle
The University of Oklahoma Health Sciences Center - University Health Club

Corresponding Author:[email protected]

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Daniel H. Leung
Texas Children's Hospital Baylor College of Medicine
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Abstract

Advanced cystic fibrosis liver disease (aCFLD) with portal hypertension develops in a minority of people (5-7.5%) with Cystic Fibrosis (CF), necessitating surgical interventions, including portosystemic shunting, gastrostomy tube placement, and in some cases, liver transplantation. This manuscript also aims to explore the different endoscopic, endovascular and surgical procedures needed to diagnose and manage aCFLD, including liver biopsy, endoscopic retrograde cholangiopancreatography, intraoperative cholangiograms, hepatic venous pressure gradient measurement and portosystemic shunt procedures in patients with aCFLD. By utilizing advanced diagnostic and surgical techniques, healthcare professionals can effectively manage aCFLD and improve patient outcomes.
17 Aug 2023Submitted to Pediatric Pulmonology
17 Aug 2023Assigned to Editor
17 Aug 2023Submission Checks Completed
17 Aug 2023Review(s) Completed, Editorial Evaluation Pending
08 Sep 2023Reviewer(s) Assigned
11 Nov 2023Editorial Decision: Revise Major