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UNDIFFERENTIATED EMBRYONAL SARCOMA OF THE LIVER: A CASE REPORT AND REVIEW OF THE LITERATURE
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  • Romero-Moreno Katherine,
  • Pineda-Garcés Catalina,
  • Muñoz-Rayo Luis,
  • Fox-Quintana Javier,
  • Gutiérrez-Montoya Jorge
Romero-Moreno Katherine
Universidad de Antioquia Departamento de Cirugia
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Pineda-Garcés Catalina
Hospital Universitario San Vicente de Paul

Corresponding Author:[email protected]

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Muñoz-Rayo Luis
Universidad de Antioquia
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Fox-Quintana Javier
Hospital Universitario San Vicente de Paul
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Gutiérrez-Montoya Jorge
Hospital Universitario San Vicente de Paul
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Abstract

Sarcomas represent less than 1% of all malignant tumors. Undifferentiated Embryonal Sarcoma (UES) of the liver is the third most common pediatric liver cancer. The main differential diagnoses are mesenchymal hamartoma, hepatoblastoma, and biliary embryonal rhabdomyosarcoma. Definitive diagnosis is confirmed by histopathology and immunohistochemical. 4-year-old male patient with fever, abdominal pain and palpable hepatomegaly was found. Magnetic Resonance Imaging (MRI) with an unifocal cystic hepatic mass, with compression and displacement of vascular structures, but without invasion; hamartoma was suspected. The management was a right hepatectomy. Immunohistochemistry studies were positive for UES. Adjuvant chemotherapy was started with a good response.