Extrarenal Wilms tumors (ERWT) are extremely rare with only isolated
case reports in the pediatric literature. As there are no specific
radiological findings suggesting ERWT, it is difficult to diagnose ERWT
accuaretely without pathological description. We present two cases who
presented with large retroperitoneal masses. Wilms tumor was not
considered in differential diagnosis as the masses were located outside
the kidney. An emphasize on ERWT’s clinical and surgical findings and
differential diagnosis were made in this report.