The whole spectrum of Hydroa vacciniforme-like lymphoproliferative
disorder in a Chinese girl
Abstract
Hydroa vacciniforme-like lymphoproliferative disorder (HVLPD) is a rare
group of chronic EBV infection-associated diseases, and usually occurs
in childhood. The prognosis of HVLPD varies. Previous researches found
that the prognosis of adults with HVLPD is worse than children. Herein,
we report a case of HVLPD in an 8-year-old girl, but the clinical course
progressed rapidly, from the classic form of HVLPD to severe HVLPD, and
finally progressed into lymphoma. Fortunately, the patient was curable
by hematopoietic stem cell transplantation. To the best of our
knowledge, this is the most complete story of HVLPD in a same patient so
far.