Important message: Due to recent site outage we are still restoring full functionality to Authorea powered sites. Please bear with us until full functionality is restored

loading page

Lamin heart disease with ventricular noncompaction and complex atrial septal arrhythmias: successful use of charge density mapping.
  • +2
  • Christoph Scharf,
  • Stefano Caselli,
  • Lam Dang,
  • Kurt Mayer,
  • Christine Attenhofer Jost
Christoph Scharf
Hirslanden Klinik im Park

Corresponding Author:[email protected]

Author Profile
Stefano Caselli
Hirslanden Klinik im Park
Author Profile
Lam Dang
Hirslanden Klinik im Park
Author Profile
Kurt Mayer
Kantonsspital Graubunden
Author Profile
Christine Attenhofer Jost
Hirslanden Klinik im Park
Author Profile

Abstract

Lamin A/C Mutations are important to recognized for therapeutic and prognostic reasons. We present the clinical cases of two sisters with Lamin A mutation presenting with complex atrial arrhythmias, atrioventricular block and ventricular arrhythmias, associated with ventricular noncompaction and abnormal pulmonary vein anatomy. The successful treatment of complex irregular atrial arrhythmias by the use of noncontact dipole density mapping and radiofrequency ablation (RFA) is described in both sisters with long-term follow up results.