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Dental abnormalities in a patient with autosomal dominant hyper-IgE syndrome: A case control study
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  • Marziyeh Heidarzadeh,
  • Atena Ramezanali Yakhchali,
  • Mohammad Gharagozlou,
  • Sepideh Darougar,
  • Zahra Chavoshzadeh,
  • Mahnaz Jamee,
  • Hossein Motedayyen
Marziyeh Heidarzadeh
Kashan University of Medical Sciences

Corresponding Author:[email protected]

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Atena Ramezanali Yakhchali
Shahid Beheshti University of Medical Sciences
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Mohammad Gharagozlou
Tehran University of Medical Sciences
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Sepideh Darougar
Islamic Azad University Tehran Medical Sciences
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Zahra Chavoshzadeh
Shahid Beheshti University of Medical Sciences
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Mahnaz Jamee
Shahid Beheshti University of Medical Sciences
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Hossein Motedayyen
Kashan University of Medical Sciences
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Abstract

Autosomal-dominant hyper-IgE (AD-HIES) is mainly characterized by eczematous dermatitis, staphylococcal skin abscesses, connective tissue defects, and elevated serum IgE. This disorder is largely associated with heterozygous dominant-negative mutations in STAT3 gene. Herein, we reported a patient with AD-HIES suffering from dental abnormality and allergic reactions.
17 May 2021Submitted to Clinical Case Reports
18 May 2021Submission Checks Completed
18 May 2021Assigned to Editor
27 May 2021Reviewer(s) Assigned
06 Jun 2021Review(s) Completed, Editorial Evaluation Pending
07 Jun 2021Editorial Decision: Revise Minor
14 Jun 20211st Revision Received
14 Jun 2021Submission Checks Completed
14 Jun 2021Assigned to Editor
14 Jun 2021Review(s) Completed, Editorial Evaluation Pending
14 Jun 2021Reviewer(s) Assigned
03 Jul 2021Editorial Decision: Revise Minor
13 Jul 20212nd Revision Received
13 Jul 2021Submission Checks Completed
13 Jul 2021Assigned to Editor
13 Jul 2021Review(s) Completed, Editorial Evaluation Pending
14 Jul 2021Reviewer(s) Assigned
22 Jul 2021Editorial Decision: Revise Minor
25 Jul 20213rd Revision Received
26 Jul 2021Assigned to Editor
26 Jul 2021Submission Checks Completed
26 Jul 2021Review(s) Completed, Editorial Evaluation Pending
27 Jul 2021Editorial Decision: Accept