Substantial Growth of Atretic Pulmonary Artery after Repair of Total
Anomalous Pulmonary Venous Connection and Congenital Diaphragmatic
Total anomalous pulmonary venous connection (TAPVC) with congenital
diaphragmatic hernia (CDH) is a disease entity with high mortality rate.
Association with atretic left pulmonary artery increased the complexity
of the anomalies. Here, we reported a newborn baby with these complex
congenital anomalies successfully treated surgically. Over 13 years
after surgery, there was substantial growth of left pulmonary artery
which was angiographically atretic at his newborn stage, which was
rarely reported. Currently, this patient is drug free and is in
functional class I of New York heart association.