A testicular and paratesticular localization of Desmoplastic Small Round
Cell Tumor: Is it a good prognostic factor?
Desmoplastic Small Round Cell Tumor (DSRCT) is an aggressive neoplasm
that classically grows in peritoneal cavity and has poor prognosis. We
describe a 13-year old boy with testicular DSRCT, treated with
orchiectomy and chemotherapy and is free of disease 96 months after
diagnosis. This is the fifth case of primary DSRCT of the testis
described in literature. Moreover, we present a literature review of 28
cases of testicular and paratesticular DSRCT and discuss these locations
as a prognostic factor.